misc. thesaurosis ; storage disease ; accumulation disease
...巨噬细胞Ly破裂 大量水解酶和 硅酸流入胞质内 诱导成纤维细胞增生并 分泌大量胶原物质,降低肺的弹性 • 贮积病(storage disease) 先天性缺乏Ly的某种水解酶,致使相应底 物不能消化而蓄积在细胞内,如Ⅱ型糖原 贮积病缺乏酸性α-葡萄糖苷酶…
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Storage disease the lung 释义:肺贮积病 thesaurosis 释义:贮积病,沉着病 Glycogenosis due inactive hepatic glycogen phosphorylase 释义:非活化肝糖原磷酸化酶性糖原贮积病 ..
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糖原贮积病 glycogen storage disease ; glycogenosis ; dextrinosis ; GSD
溶酶体贮积病 lysosomal storage disease ; lysosomal storage disoder ; LSDS
脂质贮积病 lipid storage diseases
植烷酸贮积病 [内科] phytanic acid storage disease
粘脂贮积病 mucolipidoses
粘多糖贮积病 mucopolysaccharidoses ; Other mucopolysaccharidoses
神经节苷脂贮积病 gangliosidoses
脑苷脂贮积病 cerebroside lipidosis
多糖贮积病 Mucopolysaccharidosis
·2,447,543篇论文数据,部分数据来源于NoteExpress
肝病包括黄疸、肝炎、肝硬化、肿瘤、血管阻塞、脓疮和肝糖贮积病。
Liver disorders include jaundice, hepatitis, cirrhosis, tumours, vascular obstruction, abscess, and glycogen-storage diseases.
背景- PRKAG2突变引起糖原贮积型心肌病,心室预激和传导系统退化。
Background-PRKAG2 mutations cause glycogen-storage cardiomyopathy, ventricular preexcitation, and conduction system degeneration.
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