....伴有含铁血黄素沉着症或血色病时,口服铁剂 4.伴有含铁血黄素的Kashin-Bek病 原发性血色病(hereditary hemochromatosis,HH)即遗传性血色病,其病因、临床表现和治疗原则主要是: 1、病因 血色病有原发性和继发性两类,其中H...
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...着症或血色病时,口服铁剂 4.伴有含铁血黄素的Kashin-Bek病 原发性血色病(hereditaryhemochromatosis,HH)即遗传性血色病,其病因、临床表现和治疗原则主要是: 1、病因 血色病有原发性和继发性两类,其中H...
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原发性血色病 idiopathic hemochromatosis ; primary haemochromatosis ; hereditary hemochromatosis
遗传性血色病 Hereditary Hemochromatosis ; genetic hemochromatosis ; Hereditary blood disease ; HH
研究背景遗传性血色病 hereditary haemochromatosis ; HH
继发性血色病 secondary hemochromatosis
血色病性骨关节病 osteoarticular caused by hematochromatosis
血色病性心肌病 cardiomyopathy caused by hemachromatosis
遗传性血色素沉着病 hereditaryhemochromatosis
继发性血色素沉着病 secondary hemochromatosis
获得性血色素沉着病 acquired hemochromatosis
例如,因为突变的基因可以提高铁的吸收效率,所以遗传性血色素沉着病突变可以保护带菌者不缺铁。
For example, the hereditary hemochromatosis mutation protects carriers from iron-deficiency because the mutated gene allows increased efficiency of iron absorption.
铁的过度沉淀可导致心脏增大以及类似心肌病的心力衰竭,这使得血色素沉着症成为限制性心肌病的一种形式。
The excessive deposition of iron leads to heart enlargement and failure similar to a cardiomyopathy, making hemochromatosis a form of "restrictive" cardiomyopathy.
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