骨纤维肉瘤是起源于非成骨性纤维结缔组织的一种少见恶性骨肉瘤,也是纤维源性恶性肿瘤。好发于四肢长骨干骺端或骨干,以股骨多见。原发于骨髓腔内结缔组织者,称为中央型骨纤维肉瘤,较多见。原发于骨膜的纤维组织者,称为周围型骨纤维肉瘤,较少见。继发性骨纤维肉瘤,常继发于原有骨病,如畸形性骨炎、骨纤维异样增殖症、动脉瘤样骨囊肿、慢性骨髓炎、复发的骨巨细胞瘤等。
目的:评价CT和MRI在骨纤维肉瘤中的诊断价值。
Objective:To evaluate CT and MRI in the diagnosis of fibrosarcoma of bone.
方法:回顾性分析经手术病理证实的7例骨纤维肉瘤的平片、CT和MRI表现。
Methods: The features of ct and MRI of 7 cases of fibrosarcoma of bone proved pathologically were retrospectively reviewed.
因此我们的研究与先前的研究一致,GNAS的突变在纤维性结构不良中有高度特异性,而在骨旁骨肉瘤和其它低级别骨肉瘤中即使有GNAS突变、也是很少的。
Our findings therefore support prior observations that GNAS mutations are highly specific for fibrous dysplasia and occur rarely, if ever, in parosteal and other low-grade osteosarcomas.
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