目的探讨背驼式肝移植术，解决肝豆状核变性铜代谢障碍，延长患者生存时间，改善患者的生存质量。
Objective Hepatic transplantation was performed on patients with Wilson disease to correct the disorder of copper metabolism, and to prolong lifetime and improve living quality.
目的了解肝豆状核变性误诊的原因。
Objective: To detect the reasons of misdiagnosis of Wilson disease.
比较青霉胺及锌剂治疗肝豆状核变性（HLD）的疗效及对尿铜排泄的作用。
PURPOSE To compare the efficacy and urinary copper excretion in the treatment of hepatolenticular degeneration (HLD) with penicillamine and zinc.
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