横纹肌肉瘤(RMS)可分两种不同的基本类型:(1)胚胎型(embryonal type):包括葡萄簇状及梭形细胞变型,多发生于幼和和小儿,预后相对较好。
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根据WHO肿瘤病理分类,该肿瘤分为胚胎型(embryonal rhabdomyosarcoma,ERMS)、腺泡型(alveolarrhabdomyosarcoma,ARMS)和多形型 (pleomorph...
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根据WHO肿瘤病理分类,该肿瘤分为胚胎型(embryonal rhabdomyosarcoma,ERMS)、腺泡型(alveolarrhabdomyosarcoma,ARMS)和多形型 (pleomorph...
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胚胎型腺瘤 embryonal adenoma ; embryorlaI aderloma
胚胎型横纹肌肉瘤 embryonal rhabdomyosarcoma
组织学上通常为胚胎型 embryonal rhabdomyosarcoma
该肿瘤分为胚胎型 embryonal rhabdomyosarcoma ; ERMS
胚胎期立方型细胞 cuboidal mesothelial cell
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病理诊断均为胚胎型横纹肌肉瘤。
Pathological diagnosis: All were embryonal rhabdomyosarcoma.
结论:胆道胚胎型横纹肌肉瘤极罕见,但小儿胆系恶性肿瘤多为该种肉瘤。
Conclusions: Embryonal rhabdomyosarcoma of the biliary tree, though rare, is the most common cause of biliary obstruction due to malignancy in childhood.
亚型:胚胎型(50%),小泡型累及四肢及躯干,多形性(少见)累及四肢。
Subtypes: Embryonal (50%), Alveolar involves extremities and trunk, Pleomorphic (rare) involves extremities.
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