硬斑病是局限性硬皮病的一个类型。依其皮损形态和范围的不同,又可分为斑状硬斑病、滴状硬斑病与泛发性硬斑病三种类型。 (1)斑状硬斑病:皮损多发生在腹部、背部与四肢,呈圆形或椭圆形淡红色水肿样硬斑。数年后皮损消失,遗留色素沉着。 (2)滴状硬斑病:皮损由无数粟粒状圆形斑点组成,可发生在身体任何部位,以颈、前胸和背部为多见。病变进展缓慢,硬斑可完全消退。 (3)泛发性硬斑病:皮肤损害比较广泛,呈滴状或线状,常伴有关节痛、腹痛、偏头痛及内脏损害,部分患者可发展成为系统性硬皮病。
硬斑病是一种结缔组织病,其特征是皮肤因胶原沉积过多而硬化和增厚。
Morphoea is a connective tissue disorder characterised by hardening and thickening of the skin due to an increased collagen deposition.
结果 100例患者中,51例(51%)出现线状硬皮病表现,26例(26%)出现斑块状硬斑病表现,26例(26%)出现深在性硬斑病表现,12例(12%)出现泛发性硬斑病表现,其中15例(15%)为两型混合;
Results Of a total of 100 cases, 51 (51%) were confirmed as linear scleroderma, 26 (26%) as plaque morphea, 26 (26%) as deep morphea, 12 (12%) as generalized morphea, and 15 (15%) as a mixed subtype.
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