杯状耳为耳廓上1/3的一种先天性畸形。临床表现为耳轮缘紧缩,耳轮及耳廓软骨卷曲和粘连,耳轮脚位置向前下移位,常合并有耳廓横突畸形。严重的则整个耳廓缩小,耳舟及对耳轮形态消失,整个耳廓呈管状,称之为舟状耳。这是一种较常见的耳廓先天性畸形,多发生双侧,男女比例大致相等。手术是矫正这一畸形的有效方法。手术时机可选在6岁后施行。手术治疗主要是设法增加耳轮和耳舟的长度,以使卷曲的耳廓复原。有条件时可结合招风耳的手术方法进行全面修复。手术效果较为良好。
目的探讨修复杯状耳畸形的方法和效果。
Objective To study the method and efficacy of repairing cup ear deformity.
结论:T形软骨瓣法是一种简明有效的杯状耳整形手术方法。
Conclusion This method was effective for the correction of moderate cupped ear deformity.
所查杯状耳均无耳聋病史及其它部位畸形。 结论:杯状耳的形成是由父母双方中一方杯状耳基因决定的,家系分析显示为常染色体显性遗传。
Conclusion:The family investigation suggested that the formation of cup ear was determined by the cup ear gene of an affected parent and it was an autosomal dominant inheritance.
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