临床表征除了瞳孔偏向,葡萄膜外翻,周边连黏,青光眼之外还具有特殊的色素性节结在虹彩的表面上。
Clinical manifestation with unilateral glaucoma, corectopia, ectropion uvea, peripheral anterior synechiae (pas) and characterized by pigmented nodules on the iris.
其发生青光眼的机制与虹膜前房角的发育异常有关。对先天性葡萄膜外翻合并青光眼的患者应尽早发现,早期干预和治疗。
The pathogenesis of secondary glaucoma is related to iridotrabecular dysgenesis. It is essential to detect and to treat the secondary glaucoma as early as possible.
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