在PN 患者中识别M蛋白的存在很重要,M蛋白的检测能发现 潜在的系统疾病,例如原发性淀粉样变性(Primary amyloidosis)、多发性骨髓瘤(multiple myeloma)、骨硬 化性骨髓瘤、Waldenstrom巨球蛋白血症(Waldenstrom’S macroglobulinemia)、冷沉球...
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原发性轻链淀粉样变性 primary light chain amyloidosis
目的:探讨原发性系统性淀粉样变性并发凝血因子x缺乏的临床特征、发病机制及治疗方法。
Objective: to investigate the clinical feature, pathogenesis, and therapy of Primary systemic amyloidosis with acquired factor-X deficiency.
原发性肾淀粉样变性11例,继发性肾淀粉样变性4例。
Primary kidney amyloidosis was found in 11 cases, and secondary kidney amyloidosis in 4 cases.
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