对该疾病的治疗包括维持摄入低苯丙氨酸的饮食。
The treatment includes maintaining a diet with low levels of phenylalanine.
目的总结20年对652例苯丙酮尿症患儿进行低苯丙氨酸饮食治疗经验，探讨有效的饮食控制方案。
Objective: to explore effective dietary regimens in treating phenylketonuria (PKU) after summing up 20 years practice in 652 patients.
在前三种底物条件下，当高底物浓度时，L-苯丙氨酸表现出反竞争性抑制作用； 低底物浓度时，则呈现激活作用。
As the former three substrates were employed, at high substrate concentration, L-Phe inhibited the enzyme uncompetitively and activated the enzyme at low substrate concentration.
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