下丘脑错构瘤（HH） 又称灰结节错构瘤、下丘脑神经元错构瘤，是临床极为罕见的先天性脑组织发育异常性病变。实际上，下丘脑错构瘤是发生于下丘脑下部或灰结节区的异位神经组织，而并非真性肿瘤。人群发病率约为1/5～10万，女性稍多于男性。主要于婴幼儿及儿童期发病，平均发病年龄为22个月。主要有性早熟、痴笑性癫痫、部分病例可伴有其他类型癫痫或行为异常等表现。
目的探讨儿童下丘脑错构瘤导致癫痫的手术治疗。
Objective To discuss the surgical treatment for hypothalamic hamartoma causing epilepsy in children.
目的：研究下丘脑错构瘤的CT和MRI影像表现，探讨影像学、临床及预后的关系。
Objective:To study the CT and MRI findings of hypothalamichamatomas and evaluate the correlation of imaging features, clinical symptoms and prognosis.
方法：对5例下丘脑错构瘤患者的术前头皮脑电图和术中皮层脑电图及瘤体电图进行监测，并分析讨论。
Methods:Pre operative scalp EEG, cortex EEG and the tumor body electrogram during operation were recorded in 5 patients with hypothalamic hamartoma, and the results were analyzed.
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