【正文快照】: Caroli病是一种少见的先天性非梗阻性肝内胆管扩张症,一般伴有常染色体隐性遗传性婴儿型多囊肾(RPKD)和先天性肝纤维化(CHF)。本病的诊断以往多需经皮肝穿刺活检,逆行胆道造影等侵害性技术。
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The histologic appearance in this case, coupled with the gross appearance. , was consistent with recessive polycystic kidney disease (RPKD).
在本例,肉眼和组织学表现均符合隐性遗传性多囊肾。
Here is the microscopic appearance of recessive polycystic kidney disease (RPKD). Note that the cysts fill most of the parenchyma, and it is hard to find glomeruli.
隐性遗传性多囊肾镜下见囊肿布满了实质,很难找到肾小球。
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