阿尔法1 -抗胰蛋白酶缺乏症是一种遗传疾病传播有关的风险增加肺气肿和肝脏疾病。
Alpha 1-antitrypsin deficiency is a genetically transmitted disorder associated with an increased risk of emphysema and liver disease.
过碘酸-雪夫（PAS）染色时，门脉周围的红色玻璃样小球是α-1-抗胰蛋白酶缺乏症（pi-ZZ纯合子基因型患者）的特征表现。
The periportal red hyaline globules seen here with periodic acid-Schiff (PAS) stain are characteristic for alpha-1-antitrypsin deficiency (a person with homozygous pi-ZZ genotype).
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