在相关疾病所引起的包括: Reiter syndrome, Palmoplantar keratosis ( 掌蹠角化), Subcorneal pustulosis, Inflammatory bowel disease (Crohn disease ..
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掌跖角化病 palmoplantar keratoderma ; Keratosis palmo-plantaris punctuator papules ; keratosis palmaris ; keratodermia palmaris et plantaris
掌跖角化症 keratosis palmaris et plantaris ; kertosis plmris et plntris ; palmoplantar keratoderma ; PPK
表皮松解性掌跖角化症 EPPK
弥漫性掌跖角化病 diffuse palmoplantar keratodermia ; diffuse palmoplantar keratoderma ; DPPK
表皮松解性掌跖角化病 Epidermolytic keratosis palmairs et plantaris ; Epidermolytic Palmoplantar Keratoderma ; EPPK
点状掌跖角化病 keratosis punctata palmoplantaris ; punctate palmoplantar keratoderma ; PUNCTATE PPK
钱币状掌跖角化病 keratosis palmoplantaris nummularis
水源性掌跖角化病 aquagenic palmoplantar keratoderma
性掌跖角化病 NEPPK ; diffuse palmoplantar keratoderma ; DPPK
结论:角蛋白9基因的G485A突变是导致该家系发生弥漫性掌跖角化病的原因。
Conclusion the mutation G485A found in keratin 9 gene is the disease-causing mutation in the diffuse palmoplantar keratoderma family.
本文回顾性分析了阿维A酯治疗91例角化性皮肤病(银屑病、毛发红糠疹、掌跖角化病等)的疗效和不良反应。
The effect and adverse drug reactions(ADRs )of etretinate in 91patients with keratinization, including psoriasis, pityriasis rubra pilaris, ichthyosis were analyzed retrospectively.
主要表现为色素脱失、色素沉着及掌跖过度角化,具此三联症者72例(7.35%)。
The main manifestation was hypopigment, hyperpigment, and palmoplantar Hyperkeratosis. Triad cases happened in 72 patients (7.35%).
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