是一种慢性炎症性肌病。其主要病理特点是肌浆或肌核内有管状细丝包涵体。包涵体肌炎起病隐匿,缓慢进展,首发症状约70%为下肢近端无力,也可为下肢远端、上肢或四肢均匀无力起病。肌无力可对称或不对称,随着病情进展,远端肌无力可达50%,但仅有35%其远端无力的程度达到或超过近端无力。最易受累的肌肉是肱二头肌、肱三头肌、髂腰肌、股四头肌和胫前肌,而三角肌、胸大肌、骨间肌、颈屈肌、腓肠肌及足趾屈肌受累较轻。腱反射常减低,尤以膝反射减退最为常见。
讨论:包涵体肌炎(inclusion body myositis,IBM)是一种起病隐袭,病程长,原因不明的特发性慢性炎症性肌病,多发生于中老年人,表现为缓慢持续进展的肢体肌...
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...炎;多发性肌炎;幼年型皮肌炎;无肌病型皮肌炎;无肌病型皮肌炎;包涵体肌炎;dermatomyositis;polymyositis;amyopathic dermatomyositis;amyopathic dermatomyositis;inclusion body myositis;DM;PM;ADM;EAM;JDM;IBM) 老年人原发性肝...
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...皮肌炎与多发性肌炎 (皮肌炎;多发性肌炎;幼年型皮肌炎;无肌病型皮肌炎;无肌病型皮肌炎;包涵体肌炎;dermatomyositis;polymyositis;amyopathic dermatomyositis;amyopathic dermatomyositis;inclusion body myositis;DM;PM;ADM;...
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...包涵体肌炎;dermatomyositis;polymyositis;amyopathic dermatomyositis;amyopathic dermatomyositis;inclusion body myositis;DM;PM;ADM;EAM;JDM;IBM) 联合免疫缺陷病 (严重联合免疫缺陷病;伴有血小板减少及湿疹的免疫缺陷病;共济失调毛细血管扩张症;...
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散发性包涵体肌炎 sporadic inclusion body myositis ; S-IBM
发性包涵体肌炎 sporadic inclusion body myositis ; S-IBM
及包涵体肌炎 inclusion body myositis
和包涵体肌炎 inclusion-body myositis ; IBM
包括包涵体肌炎 inclusion body myositis
还包括包涵体肌炎 inclusion body myositis
历史回顾包涵体肌炎 inclusion body myositis
⑥包涵体肌炎 inclusion body myositis
俗称披发性包涵体肌炎 S-IBM ; sporadic inclusion body myositis
目的探讨包涵体肌炎(IBM)的临床与病理特点。
Objective The study was to investigate the clinical and pathological features of inclusion body myositis(IBM).
目的探讨包涵体肌炎(ibm)的临床表现与病理特点。
Objective: To investigate the clinical and pathological features of inclusion body myositis (IBM).
近来,包涵体肌炎、皮肌炎、多发性肌炎中几种免疫细胞类型和免疫反应过程被认定。
Several immune system cell types and processes have been recently identified in muscle in inclusion body myositis dermatomyositis and polymyositis.
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