目的：探讨肺泡蛋白质沉积症(pap)的治疗。
Objective: To investigate the therapy of pulmonary alveolar proteinosis (PAP).
全肺灌洗是肺泡蛋白沉积症最安全和有效的治疗方法。
WhoLe lung irrigation is the safest and the most effective way to treat PAP.
全肺灌洗是肺泡蛋白沉积症最安全和有效的治疗方法。
WhoLe lung irrigation is the safest and the most effective way to treat PAP .
其中有两种编码突变也会引发粘脂沉积症——一种罕见的疾病。
Two of the encode mutations involved are also known to cause a rare disease called mucolipidosis.
中枢神经系统表面含铁血黄素沉积症的病因很多，详见表1。
The causes of superficial siderosis of the CNS are numerous and are listed in Table 1.
目的总结肺泡蛋白沉积症(pap)的病理特征及病理诊断要点。
Objective To study the diagnosis and pathological manifestations of pulmonary alveolar proteinosis (PAP).
结论本类脂质蛋白沉积症家系存在新的ECM 1基因突变位点。
Conclusion a new compound heterozygous mutation of ECM1 gene was identified in this LP family.
目的：总结肺泡蛋白沉积症(pap)的临床特征、诊断及治疗。
Objective: To summarize and analyze the clinical manifestations of pulmonary alveolar proteinosis (PAP) and its treatment.
目的：探讨肺泡蛋白沉积症的CT影像学表现特点，提高诊断率。
Objective: to explore the ct features of pulmonary alveolar proteinosis (PAP) and thus provide evidence to improve the accuracy of diagnosis.
目的：探讨肺泡蛋白沉积症(pap)的HRCT表现及诊断价值。
Purpose: To explore the HRCT manifestations and the diagnostic value of Pulmonary alveolar proteinosis (PAP).
目的：了解中国人群中类脂蛋白沉积症(LP)的临床表型和遗传学特点。
Objective: To explore the clinical and genetic features of lipoid proteinosis (LP) in Chinese population.
目的：探讨肺泡蛋白沉积症(pap)的X线诊断、X线分型与鉴别诊断。
Objective: To study X-ray diagnosis, classification and differential diagnosis of pulmonary alveolar proteinosis (PAP).
目的：总结肺泡蛋白沉积症(pap)患者的诊治情况，提高对本病的认识。
Objective: To improve the understanding of the diagnosis and treatment of pulmonary alveolar proteinosis (PAP).
目的研究类脂质蛋白沉积症一家系的细胞外基质蛋白1 (ECM1)基因突变。
Objective To study mutations in the extracellular matrix protein 1 (ECM1) gene in a family with lipoid proteinosis (LP).
据专家解释，这种现象非常罕见，原因是脂蛋白代谢异常或脂质沉积症，目前尚不清楚血液变色原因。
According to experts, this phenomenon caused bymetabolic abnormality of lipoprotein or lipoidosis is very rare. The reasonof the changing of the blood color is still unknown.
方法采用DNA双向测序法直接检测类脂质蛋白沉积症一家系中患者及其父母、同胞、子女的ECM1基因。
Methods Bi-directional DNA sequencing was used to detect the ECM1 gene in patients with LP as well as among their parents, siblings and children.
前言：目的：报道1例类脂蛋白沉积症家系，并对其家系成员的细胞外基质蛋白1 (ECM1)基因突变进行分析。
Objective: a Chinese family with lipoid proteinosis is reported and glycoprotein extracellular matrix protein 1 (ECM1) was identified.
如鸟有高脂肪的饮食习惯，会导致肥胖，可能会引致脂肪瘤，高脂血症(血液中的脂肪)，和肝脂沉积症(脂肪肝疾病)。
High fat in the bird's diet leads to obesity and may result in lipomas (fatty tumors), lipemia (fat in the blood), and hepatic lipidosis (fatty liver disease).
结果16例中4例表现为双肾锥体钙盐沉积症，6例表现为髓质和肾盂散在性微小结石，二者共计10例，占6 2 .5 %。
Results Calcium deposition in bilateral renal pyramids in 4 cases and scattered microcalculi in renal medulla and pelvis in 6 cases were accounted 62.5%(10/16);
CR 1基因通过清除会在老年痴呆症患者大脑中沉积的类淀粉斑，也具有保护大脑的功能。
The CR1 gene is involved in protecting the brain by clearing out amyloid plaques that can build up in Alzheimer's patients.
在动物实验中，姜黄素减少淀粉质的形成，从而减少了其易于沉积于大脑而形成老年痴呆症。
In animal studies, curcumin decreased the formation of amyloid, the stuff that makes up the brain deposits characteristic in people with Alzheimer's disease.
血色素沉着症是由于铁过度的沉积而引起的。如图所示，经过普鲁士蓝铁染色后可见该病显微镜下的表现。
Hemochromatosis, with excessive iron deposition, can occur in the heart as shown here microscopically with Prussian blue iron stain.
另一种病变为血管炎，这种血管炎往往因冷球蛋白血症、高球蛋白血症、或免疫复合物沉积而引起。
Another lesion for vasculitis, which vasculitis often due to cold hypergammaglobulinemia, high hypergammaglobulinemia, or immune complex deposition caused.
心脏穿孔和壁间造影剂沉积是选择性心血管造影严重并发症之一。
Cardiac perforation with intramural deposition of contrast agent is a severe com-plication of selective angiocardiography.
亨特氏综合症是二型粘多糖沉积病(MPSII)，是一种极其罕见的遗传性酶紊乱疾病，发病者基本只有男性。
Hunter syndrome, known more formally as mucopolysaccharidosis type II or MPS II, is an extremely rare inherited enzyme disorder that occurs almost exclusively in males.
结论：KDZOS能调节实验性高脂蛋白血症大鼠的血脂代谢，抑制肝脏脂肪沉积。
Conclusion KDZOS can adjust the blood lipid metabolism in hyperlipoproteinemia rats and restrain fatty deposition in liver.
结论：KDZOS能调节实验性高脂蛋白血症大鼠的血脂代谢，抑制肝脏脂肪沉积。
Conclusion KDZOS can adjust the blood lipid metabolism in hyperlipoproteinemia rats and restrain fatty deposition in liver.
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