丘脑是大脑中负责睡眠调控的部分，致死性家族性失眠症正是由于一种异常蛋白质“朊蛋白”在丘脑中的累积产生的。

F.F.I. is caused by anaccumulation within the thalamus — the part of the brain that controlssleep regulation — of abnormal proteins called “prions.”

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结果发现散发型克雅氏病临床诊断病例143例(44.14%)，疑似诊断病例15例(4.63%)，遗传型克雅氏病病例10例(3.09%)，致死性家族型失眠症8例(2.47%)。

Results a total of 143 probable CJD cases (44.14%) and 15 possible CJD cases (4.63%), 10 genetic CJD cases (3.09%) and 8 fatal familial insomnia (FFI) cases (2.47%) were identified.

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