一种较少见的严重先天性心脏畸形。基本病变是肺动脉瓣、肺动脉干或其分支闭锁,但以肺动脉瓣膜闭锁多见。根据有无室间隔缺损可分为室间隔完整的肺动脉闭锁和并发室间隔缺损的肺动脉闭锁两类。本病患儿在出生后均有发绀,多在婴儿期死亡。幸存者多并发有心内畸形。
肺动脉闭锁(Pulmonary Atresia,PA)是一种少见的严重紫绀型先心病,其发生闭锁的范围各有不同。听诊无特异性杂音,以往有赖于心血管造影诊断。
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...及体肺侧支_stmopen 关键词】: 肺动脉闭锁;体层摄影术 X线计算机;血管造影术 [gap=1741]Keywords】: Pulmonary artery atresia;TomographyX-ray computed;Angiography ...
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的肺动脉闭锁 pulmonary atresia ; PA
肺动脉闭锁症 pulmonary valve atresia
例肺动脉闭锁 pulmonary atresia
完整的肺动脉闭锁 PAIVS
如肺动脉闭锁 Pulmonary Atresia
间隔完整型肺动脉闭锁 pulmonary atresia with ventricular septum ; PA-IVS
对于部分如肺动脉闭锁 pulmonary atresia
肺动脉瓣闭锁 pulmonary atresia ; Pulmonary valve atresia
四联症合并肺动脉闭锁 TOF-PA
结论超声心动图可以确诊肺动脉闭锁。
Conclusions Pulmonary atresia can be diagnosed accurately by echocardiography.
组患儿中大动脉转位和室间隔完整的肺动脉闭锁手术死亡率均明显高于C组。
The death rates of D-TGA and PA/IVS in the group F were much higher than those in the group C.
其他几个重要的导管依赖型病变:主动脉缩窄、左心发育不全综合征、肺动脉闭锁。
A few other important DUCTAL-DEPENDENT lesions: Coarctation of the Aorta, Hypoplastic Left Heart Syndrome, and Pulmonary Atresia.
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