肺动脉发育不全(PAA)为较少见的先天性畸形,包括多种类型,如肺动脉主干缺如,右或左肺动脉近端缺如,左肺动脉异常起源和肺动脉缩窄等,常伴有其他心血管畸形如法洛四联症。
早期肺动脉瓣狭窄是一种可能的原因,因为假如狭窄出现的很早,右心室就不能发育,从而出现发育不全。
Early pulmonary stenosis is a possible cause because when the stenosis develops early, the right ventricle does not develop, and the right heart becomes hypoplastic.
其他几个重要的导管依赖型病变:主动脉缩窄、左心发育不全综合征、肺动脉闭锁。
A few other important DUCTAL-DEPENDENT lesions: Coarctation of the Aorta, Hypoplastic Left Heart Syndrome, and Pulmonary Atresia.
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