泛发性硬斑病罕见,其皮损的性质、发生和发展类似斑状硬斑病,但其特点为损害数目多,皮损广泛,可达数十块,分布不对称。皮损最后变为凹陷性淡白色的萎缩斑片。好发于胸腹及四肢近端,面、颈、头皮、前臂、小腿受累相对较少。虽无脏器受累,但病人可出现关节痛、腹痛、偏头痛、神经痛和精神障碍、消瘦、乏力等,少数患者可转变为系统性硬化病。
结果 100例患者中,51例(51%)出现线状硬皮病表现,26例(26%)出现斑块状硬斑病表现,26例(26%)出现深在性硬斑病表现,12例(12%)出现泛发性硬斑病表现,其中15例(15%)为两型混合;
Results Of a total of 100 cases, 51 (51%) were confirmed as linear scleroderma, 26 (26%) as plaque morphea, 26 (26%) as deep morphea, 12 (12%) as generalized morphea, and 15 (15%) as a mixed subtype.
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