...摘要: 遗传性出血性毛细血管扩张症(hereditary hemorrhagic telangiectasia,HHT)是以出血和血管畸形为特征的常染色体显性遗传病.自发性反复鼻出血是其最常见、最早出现的症状,鼻出血次数及出血量随年龄增加...
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遗传性出血性毛细血管扩张症(Hereditary Hemorrhagic Telangiectasia,HHT)就是一类经常被临床医师忽视却与肺动脉高压密切相关的疾病.
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...传性出血性(Telangiectasia,Hereditary Hemorrhagic) 【文 摘】遗传性毛细血管扩张症(hereditary hemorrhagic telangiectasia,HHT)是一种常染色体显性遗传性出血性疾病,以血管发育异常为特征,以毛细血管扩张和同一部位反复出血为临床表现..
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hereditary y hemorrhagic telangiectasia 遗传性出血性毛细管扩张
Objective: To study the treatment of nosebleed caused by hereditary hemorrhagic telangiectasia (HHT).
目的:探讨遗传性出血性毛细血管扩张症所引起鼻出血的治疗方法。
Hereditary hemorrhagic telangiectasia (HHT) or Rendu-Osler-Weber disease (ROW) is a disorder that presents with recurrent episodes of EPX.
遗传性毛细血管扩张症(HHT)或Rendu - Osler - Weber disease (ROW)是一种表现为反复出血发作的障碍。
Hereditary hemorrhagic telangiectasia is an uncommon autosomal dominant inheritance disease. 25 cases from a family were reported. The pathology, clinical presentation and treatment were discussed.
遗传出血性毛细血管扩张症为常染色体显性遗传病,临床少见,本文就其病理变化、临床特点进行讨论,探讨其治疗方法。附一家系25例分析。
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