方法对3例小儿高雪氏病的诊治过程进行回顾分析,并复习有关文献。
Methods the management of 3 children with Gaucher s disease and the literature concerned were reviewed.
目的提高对小儿高雪氏病的认识,减少误诊,选择适当的治疗方法,提高疗效。
Objective To improve the understanding, diagnosis and treatment of Gaucher's disease in childhood.
然而还很难证明这两者存在必然的联系,但是有证据表明高雪氏症确实能提高患病者的智商。
While the link is difficult to prove, there is some evidence that Gaucher disease does increase a person's IQ.
在耶路撒冷沙尔戴克医疗中心所有的高雪氏患者中,每三人中就有一人从事的工作要求平均智商达到120以上。
Around one in three people of working age who were patients of the Gaucher Clinic at the Shaare Zedek Medical Centre in Jerusalem had professions requiring an average IQ of more than 120.
即使地上有雪,高而浓密的下层植被也显露出来;雪和风也会吹落雪松、铁杉、红桤木多叶的树枝和其他的树木草料。
Even with snow on the ground, the high bushy understory is exposed; also snow and wind bring down leafy branches of cedar, hemlock, red alder, and other arboreal fodder.
表面覆盖有高丘的雪面波纹。
这个人显然是在对一个女同事说话。 他说:「雪莉,你要是想辞去工资这么高的工作,去做一个家庭妇女,那你简直是疯了。
Shirley, you’d have to be out of your skull to quit this high-paid job and become a housewife!
美泰公司针对学龄前儿童的品牌费雪也推出了“TRIO”系列品牌的积木,标榜为有着“独特的click - and - snap”技术,但看起来很像乐高。
Fisher Price, Mattel's preschool brand, launched bricks called TRIO, which boast of a "unique click-and-snap" technology but look a lot like Lego.
“过去这里会下很大的雪,积雪能有这么高,这么高,”他说一边说,一边把手比到自己的躯干和肩膀部位。他在回忆童年时期的冬天。
"We used to have snow up to here and up to here, " he said, pointing to his torso and his shoulders as he recalled a string of childhood winters.
覆雪表面具有高的反射率;土壤的反射率由高到低变化较大;植被表面和海洋的反射率较低。
Snow covered surfaces have a high albedo; the albedo of soils ranges from high to low; vegetation covered surfaces and oceans have a low albedo.
本文在切比雪夫曲线拟合方法的基础上,提出了一种高次曲线磨耗形踏面的设计方法。
On the basis of Chebyshev curve fitting method, a new method to design worn profile tread is proposed by this paper.
山沟被雪填平了,和山背一样高,成了一片片平平的雪铺的大广场。
The snow Valley is filled, and the mountain high, large square became a piece of flat snow shop.
那树有三层楼高,长得威武气派,却被细软的雪层层堆压,枝子都弯了。
That tree has three stories tall, looks mighty impressive, but was valuables layers of snow pile pressure, branches are bent.
她宛若鹅毛雪,在今夜摇曳风中,手心里高情的飘落,心尖上融化。
She like EMaoXue, tonight swaying in the wind, the hand is high feeling of falling in my heart, melting on the apex.
当霍斯汀大步走向高桌时,雪从他的斗篷上滑落,只听见他的靴子与地板的碰撞声。
Snow slid from Ser Hosteen's cloaks as he stalked toward the high table, his steps ringing against the floor.
这是因为大面积雪盖的高反射特性(北半球的冬季,雪可覆盖到40%的陆地表面)。
This is because of the highly reflective nature of snow combined with its large surface coverage (snow can cover up to 40% of the Earth's land surface during the Northern Hemisphere winter).
基于高有效位的数字计算方法和误差估计方法,对目前已提出的基于切比雪夫映射的公钥加密方法进行了改进,得到一种密钥协商协议。
Based on high effective locations algorithm and error estimate, improvement of the public-key scheme based on Chebyshev maps proposed recently was presented and a key agreement protocol was given.
如果您尝试建立一个半管是6英尺高的平地您将需要至少一个完整的泥头车装载的雪每一侧的斜坡。
If you are trying to build a half pipe that is 6 feet high on flat ground you will need at least one full dump truck load of snow for each side of the ramp.
较全面地考虑了雪盖对陆面过程的各种影响:对陆面水文的影响、对土壤热传导的影响以及雪盖的高反照率对辐射收支的影响。
A simple snow cover model has been used in LPMZD which includes effects of snow cover on soil thermodynamics and hydrology, as well as albode.
实验发现海水鱼类较淡水鱼类甲醛本底含量高,鱼雪鱼类甲醛含量比其它品种高得多。
We found the amount of instinct formaldehyde of seawater fish was higher than water fish.
风把雪飘积成高堆。
覆雪表面具有高的反射率; 土壤的反射率由高到低变化较大; 植被表面和海洋的反射率较低。
The ratio of the amplitudes of the reflected and incident waves is termed the reflectivity or reflection coefficient.
我叫高源雪。
我叫高源雪。
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