目的：探讨各种自身免疫性大疱病的临床特征和合适的治疗方法。
Objective: to study clinical features and an appropriate treatment of several kinds of autoimmune bullous diseases.
儿童获得性大疱表皮松解症（EBA）是一种自身免疫性表皮下大疱病，比较少见。
Epidermolysis bullosa acquisita(EBA) is an autoimmune subepidermal bullous disease. This disease is rare in childhood.
结果原发疾病主要为结缔组织病、大疱性皮肤病、重症药疹；死亡原因主要为严重感染和多器官功能衰竭。
Results The primary diseases were connective tissue diseases, bullous dermatoses, and severe drug eruption, and the predominant causes of death were severe infection and multiple organ failure.
认为免疫荧光检查在皮肤病诊断中具有重要地位，尤其对结缔组织类疾病和大疱类疾病更有其意义。
We considered that immunofluorescent test was important in skin disease diagnosis, especially in connective tis - Sue diseases and bullous disease.
前期的临床实验在治疗创伤，大疱性表皮松解症和鱼鳞病上已经取得了进展。
Preclinical progress has been achieved in the treatment of wounds, epidermolysis bullosa and ichthyosis.
目的评价大剂量免疫球蛋白联合糖皮质激素治疗自身免疫性大疱性皮肤病的疗效及不良反应。
Objective to assess the therapeutic effect and adverse reactions of high immunoglobulin dose in combination with glucocorticoid hormone in patients with autoimmune bullous diseases.
目的评价大剂量免疫球蛋白联合糖皮质激素治疗自身免疫性大疱性皮肤病的疗效及不良反应。
Objective to assess the therapeutic effect and adverse reactions of high immunoglobulin dose in combination with glucocorticoid hormone in patients with autoimmune bullous diseases.
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